Back to catalog Nutrigen 14 –leu for patients with isovaleric acidemia Weight of product, gr : The product is intended for dietary (therapeutic) nutrition of children of the first year of life, patients with isovalerian acidemia. Composition maltodextrins, vegetable oils (palm, coconut, soybean, corn), amino acids (L-proline, L-glutamic acid, L-lysine monohydrochloride, L-aspartic acid, L-arginine, L-serine, L-tyrosine, L-phenylalanine , L-threonine, L-glutamine, L-alanine, L-histidine, glycine, L-valine, L-isoleucine, L-tryptophan, L-methionine, L-cystine, galacto-oligosaccharides, minerals (potassium phosphate, calcium phosphate , sodium citrate, calcium hydroxide, sodium chloride, potassium citrate, magnesium oxide, ferrous sulfate, zinc sulfate, copper sulfate, manganese chloride, potassium iodate, sat sodium nitrate, chromium chloride, ammonium molybdate), emulsifier (glycerol esters of citric acid and fatty acids, mono- and diglycerides of fatty acids), polyunsaturated w-3 and w-6 fatty acids, fructooligosaccharides, vitamins (ascorbic acid, tocopherol acetate, nicotinamide, calcium pantothenate, riboflavin, pyridoxine hydrochloride, retinol acetate, thiamine hydrochloride, folic acid, phylloquinone, d-biotin, cholecalciferol, cyanocobalamin), choline bitartrate, taurine, inositol, L-carnitine tartrate, mats, anti-cyclo-acrylate, anti-tetrasin, anti-tetrasin, anti-tetras, anti-tetramino, citrate antioxidants the nutritional value Nutritional Value in 100g of product in 100ml of product Energy value, kcal / kJ 471/1971 62/260 Protein equivalent, g 14 1,8 Amino acids, g 16,6 2,2 leucine, g 0 0 Fat, g 23 3 linoleic acid, g 4,4 0,6 a-linolenic acid, g 0,36 0,05 arachidonic acid, mg 54 7 docosahexaenoic acid, mg 54 7 Carbohydrates, g 50,4 6,7 Prebiotics, g 3 0,4 galactooligosaccharides, g 2,7 0,36 fructooligosaccharides, g 0,3 0,04 Ash, g 3 0,4 Minerals: Calcium, mg 350 46 Phosphorus, mg 280 37 Potassium, mg 450 59 Sodium, mg 167 22 Magnesium mg 35 4,6 Copper, mcg 400 53 Manganese, mcg 160 21 Iron mg 5,8 0,8 Zinc, mg 3,9 0,5 Chlorides, mg 440 58 Iodine, mcg 74 10 Selenium, mcg 12 1,6 Chrome, mcg 5 0,7 Molybdenum, mcg 3 0,4 Vitamins: retinol (A), μg-eq 443 58 tocopherol (E), mg 6,2 0,8 calciferol (D), mcg 7,4 1 vitamin K, mcg 22 2,9 thiamine (B1), mcg 430 57 Riboflavin (B2), mcg 640 84 Pantothenic acid, mg 2,5 0,3 pyridoxine (B6), mcg 500 66 Niacin (PP), mg 5,6 0,7 folic acid (Bc), mcg 74 9,8 Cyanocobalamin (B12), mcg 1,2 0,16 ascorbic acid (C), mg 39,7 5,2 biotin, mcg 9,3 1,2 inositol, mg 20 2,6 choline, mg 49 6,5 carnitine mg 10,5 1,4 taurine, mg 33 4,4 Osmolality, mOsm / kg - 300 manual Important: To use strictly according to the recommendation of the doctor! The product cannot be used as a sole source of nutrition. Only for patients with isovaleric acidemia. The product is introduced into the diet gradually over 10-14 days. Initial doses of the product are 1 / 5-1 / 10 part of the required daily amount. The amount of specialized product for one feeding is determined by the doctor depending on the age and body weight and the clinical condition of the child. Direction of use: Add a specialized product to each meal. In the presence of breast milk, combine the required amount of the product diluted with water with expressed breast milk, the amount of which is determined by the doctor. In the absence of breast milk, add the required volume of the finished infant formula to the amount of product diluted with water by the doctor. The total amount of food must match the age of the child. Recommended dilution: 1 scoop without top (3.8 g) of product and 25 ml of water. Boil for at least 5 minutes all the dishes intended for feeding the child. Pour into the prepared bottle the required amount of boiled water cooled to 40-45 ° С. In the bottle of water, add the required number of measuring spoons of the product, removing the excess from the surface of the spoon with the blunt edge of the knife. After closing the bottle, shake until the powder is completely dissolved. Check the temperature of the finished mixture on the inside of the wrist. Prepare the mixture immediately before each feeding. Never use leftover mixture for the next feed! Description Before opening the package, store the product at a temperature from 0 to 25 ° С and relative air humidity not more than 75%. After opening the package, keep the product tightly closed for no more than 3 weeks in the refrigerator.