In recent years, scientific progress in the field of clinical and molecular genetics, biochemistry has made it possible to isolate from a previously undifferentiated state an extensive group of hereditary diseases associated with metabolic disorders. One of the leading methods of pathogenetic therapy of these severe conditions is dietary treatment. In accordance with modern requirements for quality and safety of medicinal products, a complete line of domestic specialized Nutrigen products has been developed for children and adults suffering from rare hereditary diseases (histidinemia, type 1 glutaric aciduria, homocystinuria, isovalerian acidemia, leucinosis or disease " maple syrup, methyl malonic and propionic acidemia, tyrosinemia) associated with impaired amino acid metabolism. Specialized products of the Nutrigen line take into account the nutritional needs of the amino acids of patients of all the above NBAO of all ages (including women in the preconceptual period and during pregnancy), which opens up broad opportunities for the implementation of adequate diet therapy of patients with NBAO.

Nutrigen 20 –leu, -ile –val
for sufferers of maple syrup
Nutrigen 70 –leu, -ile –val
for sufferers of maple syrup
Nutrigen 70 –phe
for patients with phenylketonuria
Nutrigen 14 –phe
for patients with phenylketonuria
Aphenylak 13
for patients with phenylketonuria
Nutrigen 40 –phe
for patients with phenylketonuria
Nutrigen 70 –trp, –lys
for patients with glutaric aciduria
Nutrigen 14 -ile, -met, -thr, -val
for patients with methylmalonic and propionic acidemia
Nutrigen 20 –leu
for patients with isovaleric acidemia
Aphenylak 20
for patients with phenylketonuria
Nutrigen 20 –phe
for patients with phenylketonuria
Nutrigen 70 –met
for patients with homocystinuria
Nutrigen 75
for patients with phenylketonuria
Nutrigen 20 –tyr, -phe
for patients with tyrosinemia
Nutrigen 70
for patients with phenylketonuria
Nutrigen 20 -ile, -met, -thr, -val
for patients with methylmalonic and propionic acidemia
Nutrigen 14 –leu
for patients with isovaleric acidemia
Nutrigen 14 –leu, -ile –val
for sufferers of maple syrup
Aphenylak 40
for patients with phenylketonuria
Nutrigen 14 –his
for patients with histidinemia
Nutrigen 70 –tyr, -phe
for patients with tyrosinemia
Nutrigen 14 –tyr, -phe
For patients with tyrosinemia
Nutrigen 40 –leu, -ile –val
For sufferers of maple syrup
Nutrigen 40 -ile, -met, -thr, -val
Nutrigen 14 –met
for patients with homocystinuria
Nutrigen-14-trp-lys
for patients with glutaric aciduria
Nutrigen 20 –met
for patients with homocystinuria
Nutrigen 20 –trp, –lys
for patients with glutaric aciduria
Nutrigen 40 –leu
for patients with isovaleric acidemia
Nutrigen 70 -ile, -met, -thr, -val
for patients with methylmalonic and propionic acidemia
Nutrigen 70 –leu
for patients with isovaleric acidemia
Nutrigen 40 –tyr, -phe
for patients with tyrosinemia
Nutrigen 40 –trp, –lys
for patients with glutaric aciduria
Nutrigen 30
for patients with phenylketonuria
Nutrigen 40 - met
for patients with homocystinuria
Aphenylak 15
for patients with phenylketonuria