Nutrigen 20 –leu

for patients with isovaleric acidemia

The product is intended for dietary (therapeutic) nutrition of children older than one year old, patients with isovalerian acidemia.

    maltodextrins, amino acids (L-proline, L-glutamic acid, L-lysine monohydrochloride, L-aspartic acid, L-arginine, L-serine, L-tyrosine, L-phenylalanine, L-threonine, L-glutamine, L-alanine , L-histidine, glycine, L-valine, L-isoleucine, L-tryptophan, L-methionine, L-cystine), vegetable oils (palm, coconut, soybean, corn), minerals (calcium phosphate, sodium citrate, phosphate potassium, calcium carbonate, sodium chloride, magnesium oxide, ferrous sulfate, zinc sulfate, manganese chloride, copper sulfate, potassium iodate, chromium chloride, sodium selenite, amm molybdate emulsifier (glycerol and citric acid esters of fatty acids, mono- and diglycerides of fatty acids), choline bitartrate, vitamins (ascorbic acid, tocopherol acetate, nicotinamide, calcium pantothenate, riboflavin, pyridoxine hydrochloride, retinol acetate, thiamine hydrochloride chloride, riboflavin, pyridoxine hydrochloride, retinol acetate, thiamine hydrochloride, sodium riboflavin, pyridoxine hydrochloride, retinol acetate, thiamine hydrochloride acid, phylloquinone, d-biotin, cholecalciferol, cyanocobalamin), L-carnitine tartrate, inositol, antioxidant (ascorbyl palmitate).

    Nutritional Value in 100g of product      in 100ml of product
    Energy value, kcal / kJ 471/1971 62/260
    Protein equivalent, g 14 1,8
    Amino acids, g 16,6 2,2
    leucine, g 0 0
    Fat, g 23 3
    linoleic acid, g 4,4 0,6
    a-linolenic acid, g 0,36 0,05
    arachidonic acid, mg 54 7
    docosahexaenoic acid, mg 54 7
    Carbohydrates, g 50,4 6,7
    Prebiotics, g 3 0,4
    galactooligosaccharides, g 2,7 0,36
    fructooligosaccharides, g 0,3 0,04
    Ash, g 3 0,4
    Calcium, mg 350 46
    Phosphorus, mg 280 37
    Potassium, mg 450 59
    Sodium, mg 167 22
    Magnesium mg 35 4,6
    Copper, mcg 400 53
    Manganese, mcg 160 21
    Iron mg 5,8 0,8
    Zinc, mg 3,9 0,5
    Chlorides, mg 440 58
    Iodine, mcg 74 10
    Selenium, mcg 12 1,6
    Chrome, mcg 5 0,7
    Molybdenum, mcg 3 0,4
    retinol (A), μg-eq 443 58
    tocopherol (E), mg 6,2 0,8
    calciferol (D), mcg 7,4 1
    vitamin K, mcg 22 2,9
    thiamine (B1), mcg 430 57
    Riboflavin (B2), mcg 640 84
    Pantothenic acid, mg 2,5 0,3
    pyridoxine (B6), mcg 500 66
    Niacin (PP), mg 5,6 0,7
    folic acid (Bc), mcg 74 9,8
    Cyanocobalamin (B12), mcg      1,2 0,16
    ascorbic acid (C), mg 39,7 5,2
    biotin, mcg 9,3 1,2
    inositol, mg 20 2,6
    choline, mg 49 6,5
    carnitine mg 10,5 1,4
    taurine, mg 33 4,4
    Osmolality, mOsm / kg - 300


    Use strictly according to the recommendation of the doctor!

    The product cannot be used as a sole source of nutrition.

    Only for patients with isovaleric acidemia.

    The product is introduced into the diet within 7-10 days with the gradual replacement of the specialized product for children in the first year of life with the specialized product “Nutrigen 20 –leu” for children older than a year. The volume of the previous product is reduced by 1 / 4-1 / 5 part and add the amount of new product equivalent in protein. The amount of product and liquid for dilution per feeding and the number of feedings is determined by the doctor depending on the age and body weight and the clinical condition of the child, but not less than 3 times a day.

    Direction of use:

    Dissolve the required amount of the product in a small volume of boiled water cooled to 40-45 ° С, then add the rest of the water to obtain a homogeneous liquid mixture.

    Recommended dilution: 1 scoop without top (4.2 g) of product and 25 ml of water.

    The product can be taken in the form of a thick mixture or a drink diluted with water or another liquid recommended by a doctor in a convenient concentration for the child.

    Prepare the product immediately before use.

    Never use leftover mixture for the next feed!

    • Before opening the package, store the product at a temperature from 0 to 25 ° С and relative air humidity not more than 75%.
    • After opening the package, store the product no more tightly closed for 3 weeks in the refrigerator.