Back to catalog Nutrigen 40 –leu for patients with isovaleric acidemia Weight of product, gr : The product is intended for dietary (therapeutic) nutrition of children older than one year old, patients with isovalerian acidemia. Composition amino acids (L-proline, L-glutamic acid, L-lysine monohydrochloride, L-aspartic acid, L-arginine, L-serine, L-tyrosine, L-phenylalanine, L-threonine, L-glutamine, L-alanine, L -histidine, glycine, L-valine, L-isoleucine, L-tryptophan, L-methionine, L-cystine), maltodextrins, vegetable oils (palm, coconut, soybean, corn), minerals (calcium phosphate, sodium citrate, phosphate potassium, calcium carbonate, magnesium oxide, calcium hydroxide, ferrous sulfate, zinc sulfate, manganese chloride, copper sulfate, potassium iodate, chromium chloride, sodium selenite, molybda t ammonium), emulsifier (esters of glycerol and citric acid and fatty acids, mono - and diglycerides of fatty acids), choline bitartrate, vitamins (ascorbic acid, tocopherol acetate, nicotinamide, calcium pantothenate, riboflavin, pyridoxine hydrochloride, retinol acetate, thyamine hydrochloride, retinol acetate, thymino hydrochloride folic acid, phylloquinone, d-biotin, cholecalciferol, cyanocobalamin), inositol, L-carnitine tartrate, antioxidant (ascorbyl palmitate). the nutritional value Nutritional Value in 100g of product in 100ml of product Energy value, kcal / kJ 402/1684 60/253 Protein equivalent, g 40 6 Amino acids, g 47,3 7,1 leucine, g 0 0 Fat, g 13 2 linoleic acid, g 2,6 0,4 a-linolenic acid, g 0,26 0,04 Carbohydrates, g 31,3 4,7 Minerals: Calcium, mg 900 135 Phosphorus, mg 700 105 Potassium, mg 550 83 Sodium, mg 600 90 Magnesium mg 200 30 Copper, mcg 670 101 Manganese, mcg 866 130 Iron mg 9,9 1,5 Zinc, mg 6,6 1 Chlorides, mg 880 132 Iodine, mcg 83 12 Selenium, mcg 21 3,2 Chrome, mcg 15 2,3 Molybdenum, mcg 13 2 Vitamins: retinol (A), μg-eq 633 95 tocopherol (E), mg 8,8 1,3 calciferol (D), mcg 10,5 1,6 vitamin K, mcg 32 4,8 thiamine (B1), mcg 617 93 Riboflavin (B2), mcg 917 138 Pantothenic acid, mg 3,6 0,5 pyridoxine (B6), mcg 717 108 Niacin (PP), mg 8 1,2 folic acid (Bc), mcg 105 16 Cyanocobalamin (B12), mcg 1,8 0,3 ascorbic acid (C), mg 57 8,6 biotin, mcg 13 2 inositol, mg 100 15 choline, mg 120 18 carnitine mg 60 9 manual Important: Use strictly according to the recommendation of the doctor! The product cannot be used as a sole source of nutrition. Only for patients with isovaleric acidemia. The product is introduced into the diet within 7-10 days with the gradual replacement of the specialized product for children in the first year of life with the specialized product “Nutrigen 40 –leu” for children older than a year. The volume of the previous product is reduced by 1 / 4-1 / 5 part and add the amount of new product equivalent in protein. The amount of product and liquid for dilution per feeding and the number of feedings is determined by the doctor depending on the age and body weight and the clinical condition of the child, but not less than 3 times a day. Direction of use: Dissolve the required amount of the product in a small volume of boiled water cooled to 40-45C, then add the remaining part of the water to obtain a homogeneous liquid mixture. Recommended dilution: 1 scoop without top (4.7 g) of the product and 30 ml of water. The product can be taken in the form of a thick mixture or a drink diluted with water or another liquid recommended by a doctor in a convenient concentration for the child. Prepare the product immediately before use. Never use leftover mixture for the next feed! Description Before opening the package, store the product at a temperature from 0 to 25 ° С and relative air humidity not more than 75%. After opening the package, store the product for no more than 3 weeks tightly closed in the refrigerator.