Nutrigen 40 –leu, -ile –val

For sufferers of maple syrup

The product is intended for dietary therapeutic nutrition of children over one year of age suffering from maple syrup disease.

    maltodextrins, amino acids (L-lysine monohydrochloride, L-aspartic acid, L-proline, L-glutamic acid, L-arginine, L-serine, L-threonine, L-phenylalanine, L-alanine, L-tyrosine, L-glutamine , glycine, L-histidine, L-cystine, L-methionine, L-tryptophan), vegetable oils (palm, coconut, soybean, corn), minerals (calcium phosphate, sodium citrate, potassium phosphate, calcium carbonate, magnesium oxide, ferrous sulfate, zinc sulfate, manganese chloride, copper sulfate, potassium iodate, chromium chloride, sodium selenite, ammonium molybdate), corn starch, emulsate op (esters of glycerol and citric acid and fatty acids, mono- and diglycerides of fatty acids), choline bitartrate, vitamins (ascorbic acid, tocopherol acetate, nicotinamide, calcium pantothenate, riboflavin, pyridoxine hydrochloride, retinol acetate, thiamine hydrochloride, chitol nitride, chloramine, pyrofluxamine, pyridoxine hydrochloride, retinol acetate, thiamine hydrochloride, chitramine , d-biotin, cholecalciferol, cyanocobalamin), L-carnitine tartrate, inositol, antioxidant (ascorbyl palmitate).

    Nutritional Value in 100g of product      in 100ml of product
    Energy value, kcal / kJ 401/1681 60/252
    Protein equivalent, g 40 6
    Amino acids, g 47,5 7,1
    valine, g 0 0
    isoleucine, g 0 0
    leucine, g 0 0
    Fat, g 13 2
    linoleic acid, g 2,6 0,4
    a-linolenic acid, g 0,26 0,04
    Carbohydrates, g 31,1 4,7
    Minerals:    
    Calcium, mg 900 135
    Phosphorus, mg 700 105
    Potassium, mg 550 83
    Sodium, mg 600 90
    Magnesium mg 200 30
    Copper, mcg 670 101
    Manganese, mcg 866 130
    Iron mg 9,9 1,5
    Zinc, mg 6,6 1
    Chlorides, mg 1000 150
    Iodine, mcg 83 12
    Selenium, mcg 21 3,2
    Chrome, mcg 15 2,3
    Molybdenum, mcg 13 2
    Vitamins:    
    retinol (A), μg-eq 633 95
    tocopherol (E), mg 8,8 1,3
    calciferol (D), mcg 10,5 1,6
    vitamin K, mcg 32 4,8
    thiamine (B1), mcg 617 93
    Riboflavin (B2), mcg 917 138
    Pantothenic acid, mg 3,6 0,5
    pyridoxine (B6), mcg 717 108
    Niacin (PP), mg 8 1,2
    folic acid (Bc), mcg 105 16
    Cyanocobalamin (B12), mcg      1,8 0,3
    ascorbic acid (C), mg 57 8,6
    biotin, mcg 13 2
    inositol, mg 100 15
    choline, mg 120 18
    carnitine mg 60 9

    Important:
    Use strictly according to the recommendation of the doctor!

    The product cannot be used as a sole source of nutrition.

    Only for patients with maple syrup disease.

    The product is introduced into the diet within 7-10 days with the gradual replacement of the specialized product for children in the first year of life with the specialized product “Nutrigen 40 –leu, -ile –val” for children over one year old. The volume of the previous product is reduced by 1 / 4-1 / 5 part and add the amount of new product equivalent in protein. The amount of product and liquid for dilution per feeding and the number of feedings is determined by the doctor depending on the age and body weight and the clinical condition of the child, but not less than 3 times a day.

    Direction of use:

    Dissolve the required amount of the product in a small volume of boiled water cooled to 40-450C, then add the remaining part of the water to obtain a homogeneous liquid mixture.

    Recommended dilution: 1 scoop without top (4.7 g) of the product and 30 ml of water.

    The product can be taken in the form of a thick mixture or a drink diluted with water or another liquid recommended by a doctor in a convenient concentration for the child.

    Prepare the mixture immediately before each use.

    Never use leftover mixture for the next use!

    • Before opening the package, store the product at a temperature from 0 to 25 ° С and relative air humidity not more than 75%.
    • After opening the package, store the product no more tightly closed for 3 weeks in the refrigerator.